Background: Numerous malignancies, both benign and malignant is hosted by the sinonasal cavity that poses a diagnostic and therapeutic challenge to otolaryngologist and pathologists. One of the extremely rare neoplasm of the sinonasal cavity is secretory carcinoma (SC), previously called, mammary analogue secretory carcinoma (MASC). Majority of MASCs are localized to the parotid and salivary glands however, it is rarely documented in the sinonasal tract. Herein, we review the reported cases and report a twenty-one-year-old female patient presented to our ear, nose & throat outpatient department of tertiary care center as a polyp in the nasal cavity initially, which was excised on first diagnoses with normal histopathology (H/P). However, a year later she has a recurrence with an invasive course, followed by surgical exploration and confirmed as “Secretory Carcinoma” (SC) on histopathology, immunohistochemistry & genetic confirmation. At two-years follow-up, the patient has no clinical and radiological signs of recurrence. Aim: this review aims to outline the demographic, clinicopathologic, and confirmatory (radiologic, histopathologic, and immunohistochemistry) findings of the published cases. Methods: PubMed, Google Scholar, and MEDLINE search done with search words such as, secretary carcinoma, sinonasal tract, mammary analogue secretary carcinoma. Results: Total eight case including our case included in this review. The male/female ratio of occurrence of the SC of the sinonasal cavity was 3:5 (34.5:62.5%). Majority of the cases (7/8) reported in middle and old age group except one as reported in a 12 years old child. Equal case distribution among smoker ad non-smoker patients. The common symptoms were nasal obstruction, nasopharyngeal secretions, presence of mass, epistaxis and hyposmia. All cases were characterized by the presence of the ETV6-NTRK3 fusion transcript and / or rearrangement of ETV6 gene. Surgical excision with chemo/radiotherapy was the management considered in majority of the cases with good outcome. Almost all eight cases (100%) has no signs of recurrence both clinical and radiologically at a mean follow-up period of one year. Conclusion: Secretary carcinoma of the sinonasal tract is a new entity. More cases / studies are required to know the demographic, clinicopathologic nature, & prognosis of this newly emerging carcinoma.