Extraskeletal myxoid chondrosarcoma is a rare malignant soft tissue tumor of uncertain differentiation, constituting less than 3% of all soft tissue sarcomas. This low grade malignant tumor with high recurrence and metastatic potential, occurs predominantly in proximal extremities and limb girdles of males with thigh being the most common location. Here we present a case in a 35 years old female, who presented with pain and large swelling of around 8cm in lateral side of left leg since five months. Wide local excision of the tumor was done and on histopathology a diagnosis of Extraskeletal myxoid chondrosarcoma was rendered. On Immunohistochemistry the tumor cells showed reactivity for Vimentin, S100 and NSE and was non-reactive for CK. Thus our histopathological diagnosis was reconfirmed by immunohistochemistry. Despite high incidence of local recurrence and metastasis, ESMC has an excellent overall survival rate.