Background: The clinical heterogeneity of Rare bleeding Disorders (RBDs) associated with their rarity is a significant barrier to enhancing their deeper knowledge. Diagnosis, classification and adequate treatment of these disorders has been hampered by the variable clinical presentation and difficulty in recognizing affected patients, difficulty in collecting longitudinal clinical data and limits of laboratory assays. The objective this study is to evaluate the distribution of RBDs amongst inherited bleeding disorders and approach to RBDswith clinical evaluation & lab diagnosis. Materials and methods: This is a Retrospective study of rare bleeding disorders obtained from the cases referred from Karnataka Haemophilia Society to the Haematology section of department of Pathology, JJM Medical College, Davangere from June 2006 to June 2011. Results: Out of the total of 400 patients of inherited bleeding disorders referred, 23 were diagnosed of RBDs which included 11 cases of factor XIII deficiency, 4 of Hypofibrinogenemia, 3 of Afibrinogenemia, one each of factor II,V,VII,XI deficiency. Conclusion: RBDs poses significant social problem in our country. Lab diagnosis of these disorders is complex but basic coagulation set up with high clinical suspicion can take up the challenge of diagnosing these disorders.