Ectopic pancreas is an abnormal condition of embryological origin. The relationship of ectopic pancreatic tissue associated with choledochal cyst is extremely rare condition. The most commonly reported cases of ectopic pancreatic tissue are located in the upper GI (gastrointestinal) tract with most frequent site is stomach, followed by the duodenum and the jejunum. The clinical implication of the presence of ectopic pancreas in the choledochal cyst is remain unclear but it’s predicted risk for developing futher complications, especially pancreatic malignancy should always be considered. Ectopic pancreatic tissue can be diagnosed at all ages, males are frequently associated but a higher incidence of ectopic pancreas in the gallbladder is found in females and most incidence lies between the thirty to sixty years of life. The purpose of the present case is to present the clinical, and histopathological features of ectopic pancreatic tissue associated with choledochal cyst of 21 years old female. However, the basic concept of occurrence of ectopic pancreatic tissue is contentious. To conclude, the ectopic pancreatic tissue associated with choledochal cyst may be an evidence of its embryological association and it’s greater risk for development of further complications, especially development of pancreatic malignancy. The present case should be considered for long term follow up as only doing cystectomy will not provide full protection against the development of pancreatic malignancy.