Ciliated hepatic foregut cysts (CHFCs) are a benign cyst of the liver with a ciliated coating. It is an extremely rare solitary cystic lesion. In this paper, we present a case of CHFCs in a 41-year-old woman. Our goal was to insist by the report of this clinical observation and the review of the literature on the main issue of this pathology which is to ensure a regular and rigorous monitoring of patients with CHFCs or a radical surgical treatment to anticipate or avoid malignant complications.