Dens invaginatus is a tooth malformation resulting from an infolding of the dental papilla at the time of tooth development. The deep infolding of enamel and dentin are seen in the affected tooth. Maxillary lateral incisors are commonly affected tooth and bilateral occurrence is rare. It shows a broad spectrum of morphologic variations and it usually results in pulpal necrosis. Root canal therapy may undergo severe problems due to its complex anatomy of teeth. This review addresses the etiology, clinical and radiographic features of taurodontism, its association with various anomalies, as well as important considerations in various areas of expertise dental treatments of such teeth.