Glomus tumor is a rare hamartoma, most often seen in young females, typically in the subungual region. Extradigital sites like the middle ear are uncommon and often misdiagnosed due to nonspecific presentation. Glomus tumor is a rare (7%) benign neoplasm arising from the glomus body, a neuromyoarterial structure involved in thermoregulation. We present a rare case of glomus tumor in the middle ear.